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Property "Has-20abstract" (as page type) with input value "-5B-5BImage:MITOEAGLE-2Dlogo.jpg-7Cleft-7C100px-7Clink=http:-2F-2Fwww.mitoglobal.org-2Findex.php-2FMITOEAGLE-7CCOST-20Action-20MitoEAGLE-5D-5D-0AL-2DCarnitine-20was-20discovered-20more-20than-20hundred-20years-20ago-20by-20the-20Latvian-20biochemist-20R.-20Krimberg-20-5B1-5D,-20but-20it-20took-20more-20than-20half-20a-20century-20until-20its-20role-20in-20long-2Dchain-20fatty-20acid-20oxidation-20by-20mitochondria-20was-20described.-20In-20the-201970-2D80s,-20the-20cases-20of-20inborn-20errors-20in-20carnitine-20metabolism-20were-20reported-20and-20details-20of-20the-20enzymes-20and-20transporters-20of-20the-20carnitine-20system-20delineated-20at-20the-20genetic-20level.-20Nowadays-20L-2Dcarnitine-20is-20a-20very-20popular-20food-20supplement-20due-20to-20its-20safety-20profile-20and-20suggested-20effects-20on-20energy-20metabolism-20pathways-20-5B2-5D.-20L-2Dcarnitine-20is-20frequently-20used-20in-20cocktails-20of-20food-20supplements-20that-20are-20believed-20to-20increase-20fatty-20acid-20metabolism,-20eliminate-20body-20fat-20and-20increase-20fitness.-20However,-20the-20scientific-20evidence-20supporting-20its-20efficacy-20is-20inconclusive-20and-20the-20body-20weight-2Dreducing-20effect-20of-20L-2Dcarnitine-20supplementation-20has-20not-20been-20proven-20clinically.-20In-20addition,-20L-2Dcarnitine-20is-20not-20considered-20as-20a-20doping-20agent,-20but-20it-20has-20been-20shown-20to-20positively-20impact-20the-20recovery-20process-20after-20exercise.-20To-20drive-20the-20processes-20of-20fatty-20acid-20metabolism,-20excessive-20concentrations-20of-20L-2Dcarnitine-20should-20reach-20the-20cellular-20mitochondria,-20but-20its-20bioavailability-20during-20normal-20homeostasis-20is-20quite-20low.-20The-20intake-20of-20high-20doses-20of-20L-2Dcarnitine-20impacts-20body-20levels-20of-20L-2Dcarnitine-20metabolites,-20long-2Dchain-20acylcarnitines-20and-20trimethylamine-2DN-2Doxide.-20The-20increase-20in-20the-20tissue-20and-20plasma-20pools-20of-20long-2Dchain-20acylcarnitines-20has-20been-20linked-20to-20the-20disturbed-20energy-20metabolism-20and-20development-20of-20insulin-20resistance,-20as-20well-20as-20increased-20ischemia-2Dreperfusion-20damage-20-5B3-5D.-20Elevated-20trimethylamine-2DN-2Doxide-20levels-20impair-20pyruvate-20and-20fatty-20acid-20oxidation-20in-20cardiac-20mitochondria-20and-20predict-20an-20increased-20risk-20of-20cardiometabolic-20diseases-20and-20an-20increased-20incidence-20of-20major-20adverse-20cardiac-20events-20-5B4-5D.-20More-20studies-20are-20needed-20to-20evaluate-20the-20hypothesis-20of-20long-2Dchain-20acylcarnitines-20and-20trimethylamine-2DN-2Doxide-20as-20novel-20diagnostic-20markers-20and-20to-20use-20L-2Dcarnitine-2Drelated-20pathway-20regulation-20to-20treat-20cardiovascular-20diseases-20and-20diabetes." contains invalid characters or is incomplete and therefore can cause unexpected results during a query or annotation process.

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