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• McKenzie 2006 J Mol Biol
  ...(2006) Mitochondrial respiratory chain supercomplexes are destabilized in Barth Syndrome patients. J Mol Biol 361:462-9. ...subunit levels. We propose that the loss of mature cardiolipin species in Barth Syndrome results in unstable respiratory chain supercomplexes, thereby affe
  2 KB (305 words) - 18:52, 16 January 2021
• Boltzmann 1896 Verlag Johann Ambrosius Barth, Leipzig
  ...zmann Ludwig (1896) Vorlesungen über Gastheorie I. Verlag Johann Ambrosius Barth, Leipzig:204 pp. |journal=Verlag Johann Ambrosius Barth, Leipzig
  819 bytes (103 words) - 10:33, 6 July 2022
• Gebert 2009 Curr Biol
  ...ardiolipin involved in outer-membrane protein biogenesis: implications for Barth syndrome. Curr Biol 19:2133-9. ...mitochondrial outer membrane and bear implications for the pathogenesis of Barth syndrome.
  2 KB (258 words) - 18:32, 16 January 2021
• Ostwald 1912 Verlag von Johann Ambrosius Barth
  |title=Ostwald W (1912) Die Energie. Verlag von Johann Ambrosius Barth Leipzig:167 pp. |journal=Verlag von Johann Ambrosius Barth
  1 KB (171 words) - 13:43, 2 April 2018
• Petit 2018 MiP2018
  ...nd human Tafazzin-deficient cells with dirupted mitochondrial homeostasis (Barth syndrome cell model). ...erre JP, Godard F, Sardin E, Bouhier M, Le Guedard M, Kucharczyk R, Testet E, Di Rago JP, Tribouillard-Tanvier D, Petit PX
  3 KB (466 words) - 09:37, 20 August 2018
• Sprenger 2018 EMBO Mol Med
  ...Wani G, Hesseling A, König T, Patron M, MacVicar T, Ahola S, Wai T, Barth E, Rugarli EI, Bergami M, Langer T (2018) Loss of the mitochondrial i-AAA pro ...Wani G, Hesseling A, Koenig T, Patron M, MacVicar T, Ahola S, Wai T, Barth E, Rugarli EI, Bergami M, Langer T
  2 KB (282 words) - 13:23, 17 April 2019
• Petit 2013 Abstract MiP2013
  ...le=Petit PX (2013) The cardiolipin defect linked to a tafazzin mutation in Barth syndrome disturbs mitochondrial metabolism, alters apoptosis and autophagic ...issing link between receptors at the plasma membrane and the mitochondria. Barth syndrome-derived lymphoblasts also exhibit a subtle increase in ROS product
  4 KB (639 words) - 11:21, 28 April 2017
• Petit 2017 MiP2017
  |title=[[Image:PetitP.jpg|left|90px|Patrice Petit]] Barth syndrome cardiolipin alterations linked to tafazzin mutations lead to apopt ...in research providing some clues to better understand the link between the Barth syndrome pathology and the mitochondrial dysfunctions exhibiting defects in
  3 KB (474 words) - 13:57, 16 October 2017
• Schatton 2017 J Cell Biol
  ...H, Mourier A, Nemazanyy I, Pessia A, Zentis P, Corona T, Kondylis V, Barth E, Schauss AC, Velagapudi V, Rugarli EI (2017) CLUH regulates mitochondrial m ...H, Mourier A, Nemazanyy I, Pessia A, Zentis P, Corona T, Kondylis V, Barth E, Schauss AC, Velagapudi V, Rugarli EI
  2 KB (307 words) - 08:18, 28 March 2018
• Kutschka 2023 Basic Res Cardiol
  ...Activation of the integrated stress response rewires cardiac metabolism in Barth syndrome. https://doi.org/10.1007/s00395-023-01017-x |abstract=Barth Syndrome (BTHS) is an inherited cardiomyopathy caused by defects in the mit
  3 KB (398 words) - 17:47, 14 November 2023
• Nickel 2018 IOC130
  ...ndrial calcium uptake precede defects of the respiratory chain in X-linked Barth syndrome cardiomyopathy. |authors=Nickel A, Bertero E, Kohlhaas M, Hohl M, Krug C, Mueller A*, Lafontaine M, Lancaster R, Kappl R
  1 KB (193 words) - 14:12, 7 March 2020
• Morad 2016 J Lipid Res
  ...ougall MR, Fox TE, Tan SF, Feith DJ, Loughran TP Jr, Kester M, Claxton DF, Barth BM, Deering TG, Cabot MC (2016) Ceramide-tamoxifen regimen targets bioenerg ...ougall MR, Fox TE, Tan SF, Feith DJ, Loughran TP Jr, Kester M, Claxton DF, Barth BM, Deering TG, Cabot MC
  3 KB (367 words) - 13:08, 24 February 2020
• Le 2020 J Biol Chem
  ...Li Puma Lance C, Mulligan Christopher M, Heuberger Adam L, Prenni Jessica E, Claypool Steven M, Chatfield Kathryn C, Sparagna Genevieve C, Chicco Adam |abstract=Barth syndrome (BTHS) is a mitochondrial myopathy resulting from mutations in the
  3 KB (426 words) - 12:52, 5 January 2022
• Oemer 2018 Proc Nat Acad Sci U S A
  ...er L, Muigg K, Krumschnabel G, Watschinger K, Sailer S, Lindner H, Gnaiger E, Wortmann SB, Werner ER, Zschocke J, Keller MA (2018) The molecular structu |editor=Gnaiger E
  2 KB (360 words) - 12:48, 27 December 2021
• Affinity of reaction
  Communicated by [[Gnaiger E]] 2018-12-27 (last update 2019-01-04) ...nschaftliche Abhandlungen von Hermann von Helmholtz. 3 vols. Leipzig: J.A. Barth, 1882-95.) [8]
  7 KB (902 words) - 12:40, 11 March 2024
• Calzia 2013 Abstract MiP2013
  |title=Calzia E, Wagner K, Wagner F, Groeger M, Matallo J, McCook O, Wachter U, Vogt J, Rad |authors=Calzia E, Wagner K, Wagner F, Groeger M, Matallo J, McCook O, Wachter U, Vogt J, Rad
  6 KB (896 words) - 17:09, 9 November 2017
• MiPNet17.08 IOC68 Schroecken AT
  |[[Albertini E|Albertini Eva]] |[[Barth S|Barth Sonja]]
  15 KB (2,242 words) - 14:11, 21 July 2020
• Laner 2013 Mitochondr Physiol Network MiP2013
  ...ttp://www.mitophysiology.org|MiPsociety]]Laner V, Bidaurratzaga E, Gnaiger E, eds (2013) Comparative Mitochondrial Physiology. MiP2013. Mitochondr Physi | [[Gnaiger E]], Chair, MiP''society''||Medical University Innsbruck, AT||[[Gnaiger 2013
  26 KB (3,454 words) - 12:10, 23 January 2019
• MitoFit SC 2016 Programme information
  ::::* [[Gnaiger 2014 MitoPathways |'''Gnaiger E''']] (AT) SUIT protocols - MitoPathways 2007-2016. ...DatLab |'''Gradl L, Capek O, Plattner C, Droescher S, Doerrier C, Gnaiger E''']] (ORO) '''Release of DatLab 7''' - new dimensions with MitoFit quality
  34 KB (4,472 words) - 11:55, 12 March 2024
• Gnaiger 2019 MitoFit Preprints
  |title=Gnaiger E, Aasander Frostner E, Abdul Karim N, Abdel-Rahman EA, Abumrad NA, Acuna-Castroviejo D, Adiele RC |editor=[[Gnaiger E]]
  38 KB (5,252 words) - 08:27, 8 January 2023

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